HAEM5:Acute megakaryoblastic leukaemia: Difference between revisions

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<blockquote class='blockedit'>{{Box-round|title=v4:Clinical Features|The content below was from the old template. Please incorporate above.}}
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*Common manifestations include cytopenias (often thrombocytopenia)<ref name=":0" />.
*Common manifestations include cytopenias (often thrombocytopenia)<ref name=":0" />.
*An association between acute megakaryoblastic leukemia and mediastrinal germ cell tumors has been described<ref>{{Cite journal|last=Nichols|first=C. R.|last2=Roth|first2=B. J.|last3=Heerema|first3=N.|last4=Griep|first4=J.|last5=Tricot|first5=G.|date=1990|title=Hematologic neoplasia associated with primary mediastinal germ-cell tumors|url=https://www.ncbi.nlm.nih.gov/pubmed/2158625|journal=The New England Journal of Medicine|volume=322|issue=20|pages=1425–1429|doi=10.1056/NEJM199005173222004|issn=0028-4793|pmid=2158625}}</ref>.
*An association between acute megakaryoblastic leukemia and mediastrinal germ cell tumors has been described<ref>{{Cite journal|last=Nichols|first=C. R.|last2=Roth|first2=B. J.|last3=Heerema|first3=N.|last4=Griep|first4=J.|last5=Tricot|first5=G.|date=1990|title=Hematologic neoplasia associated with primary mediastinal germ-cell tumors|url=https://www.ncbi.nlm.nih.gov/pubmed/2158625|journal=The New England Journal of Medicine|volume=322|issue=20|pages=1425–1429|doi=10.1056/NEJM199005173222004|issn=0028-4793|pmid=2158625}}</ref>.


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==Sites of Involvement==
==Sites of Involvement==
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* Individual Region Genomic Gain/Loss/LOH
* Individual Region Genomic Gain/Loss/LOH
* Characteristic Chromosomal Patterns
* Characteristic Chromosomal Patterns
* Gene Mutations (SNV/INDEL)}}
* Gene Mutations (SNV/INDEL)}}</blockquote>


Diagnosis
Diagnosis
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*The prognosis of AMKL is usually poorer than that of other AML types,  [[HAEM5:Acute myeloid leukaemia with RBM15::MRTFA fusion]], and [[HAEM5:Myeloid proliferations associated with Down syndrome]]<ref name=":0" /><ref>{{Cite journal|last=Oki|first=Yasuhiro|last2=Kantarjian|first2=Hagop M.|last3=Zhou|first3=Xian|last4=Cortes|first4=Jorge|last5=Faderl|first5=Stefan|last6=Verstovsek|first6=Srdan|last7=O'Brien|first7=Susan|last8=Koller|first8=Charles|last9=Beran|first9=Miloslav|date=2006|title=Adult acute megakaryocytic leukemia: an analysis of 37 patients treated at M.D. Anderson Cancer Center|url=https://www.ncbi.nlm.nih.gov/pubmed/16123215|journal=Blood|volume=107|issue=3|pages=880–884|doi=10.1182/blood-2005-06-2450|issn=0006-4971|pmid=16123215}}</ref>.
*The prognosis of AMKL is usually poorer than that of other AML types,  [[HAEM5:Acute myeloid leukaemia with RBM15::MRTFA fusion]], and [[HAEM5:Myeloid proliferations associated with Down syndrome]]<ref name=":0" /><ref>{{Cite journal|last=Oki|first=Yasuhiro|last2=Kantarjian|first2=Hagop M.|last3=Zhou|first3=Xian|last4=Cortes|first4=Jorge|last5=Faderl|first5=Stefan|last6=Verstovsek|first6=Srdan|last7=O'Brien|first7=Susan|last8=Koller|first8=Charles|last9=Beran|first9=Miloslav|date=2006|title=Adult acute megakaryocytic leukemia: an analysis of 37 patients treated at M.D. Anderson Cancer Center|url=https://www.ncbi.nlm.nih.gov/pubmed/16123215|journal=Blood|volume=107|issue=3|pages=880–884|doi=10.1182/blood-2005-06-2450|issn=0006-4971|pmid=16123215}}</ref>.


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==Individual Region Genomic Gain / Loss / LOH==
==Individual Region Genomic Gain / Loss / LOH==
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==Characteristic Chromosomal Patterns==
==Characteristic Chromosomal Patterns==
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*No unique chromosomal abnormality is associated with AMKL.
*No unique chromosomal abnormality is associated with AMKL.
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*Isochromosome 12p is often observed in young males with mediatinal germ tumors and AMKL<ref>{{Cite journal|last=Orazi|first=A.|last2=Neiman|first2=R. S.|last3=Ulbright|first3=T. M.|last4=Heerema|first4=N. A.|last5=John|first5=K.|last6=Nichols|first6=C. R.|date=1993|title=Hematopoietic precursor cells within the yolk sac tumor component are the source of secondary hematopoietic malignancies in patients with mediastinal germ cell tumors|url=https://www.ncbi.nlm.nih.gov/pubmed/8389653|journal=Cancer|volume=71|issue=12|pages=3873–3881|doi=10.1002/1097-0142(19930615)71:123.0.co;2-1|issn=0008-543X|pmid=8389653}}</ref>.
*Isochromosome 12p is often observed in young males with mediatinal germ tumors and AMKL<ref>{{Cite journal|last=Orazi|first=A.|last2=Neiman|first2=R. S.|last3=Ulbright|first3=T. M.|last4=Heerema|first4=N. A.|last5=John|first5=K.|last6=Nichols|first6=C. R.|date=1993|title=Hematopoietic precursor cells within the yolk sac tumor component are the source of secondary hematopoietic malignancies in patients with mediastinal germ cell tumors|url=https://www.ncbi.nlm.nih.gov/pubmed/8389653|journal=Cancer|volume=71|issue=12|pages=3873–3881|doi=10.1002/1097-0142(19930615)71:123.0.co;2-1|issn=0008-543X|pmid=8389653}}</ref>.


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==Gene Mutations (SNV / INDEL)==
==Gene Mutations (SNV / INDEL)==
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==Epigenomic Alterations==
==Epigenomic Alterations==
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==Genetic Diagnostic Testing Methods==
==Genetic Diagnostic Testing Methods==