HAEM5:Systemic EBV-positive T-cell lymphoma of childhood: Difference between revisions

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** The WHO 5th edition and International Consensus Classification note that cytogenetic abnormalities favor a diagnosis of SEBVTCL over EBV-positive nonfamilial HLH.<ref name=":3" /><ref name=":0" />  
** The WHO 5th edition and International Consensus Classification note that cytogenetic abnormalities favor a diagnosis of SEBVTCL over EBV-positive nonfamilial HLH.<ref name=":3" /><ref name=":0" />  
** Primary/familial EBV-positive HLH can be excluded by family history and genetic analysis<ref name=":10" />
** Primary/familial EBV-positive HLH can be excluded by family history and genetic analysis<ref name=":10" />
* TCR-gene rearrangements can be detected via PCR or NGS methods. Cytogenetic abnormalities can be detected with karyotype and/or chromosome microarray (CMA).
* TCR-gene rearrangements can be detected via PCR or NGS methods. Cytogenetic abnormalities can be detected with karyotype and chromosome microarray (CMA).


== Familial Forms ==
== Familial Forms ==