CNS5:Table of Contents
Revision as of 12:03, 20 October 2026 by Richard.Glen (talk | contribs)
Gliomas, glioneuronal tumours, and neuronal tumours (Overview Page Link Complete )
Gliomas, glioneuronal tumours, and neuronal tumours Adult-type diffuse gliomas - CNS5:Astrocytoma, IDH-mutant Incomplete - CNS5:Oligodendroglioma, IDH-mutant and 1p/19q-codeleted Incomplete - CNS5:Glioblastoma, IDH-wildtype Incomplete Paediatric-type diffuse low-grade gliomas - CNS5:Diffuse astrocytoma, MYB- or MYBL1-altered Incomplete - CNS5:Angiocentric glioma Incomplete - CNS5:Polymorphous low-grade neuroepithelial tumour of the young Incomplete - CNS5:Diffuse low-grade glioma, MAPK pathway-altered Incomplete Paediatric-type diffuse high-grade gliomas - CNS5:Diffuse midline glioma, H3 K27-altered Complete - CNS5:Diffuse hemispheric glioma, H3 G34-mutant Incomplete - CNS5:Diffuse paediatric-type high-grade glioma, H3-wildtype and IDH-wildtype Incomplete - CNS5:Infant-type hemispheric glioma Incomplete Circumscribed astrocytic gliomas - CNS5:Pilocytic astrocytoma Incomplete - CNS5:High-grade astrocytoma with piloid features Incomplete - CNS5:Pleomorphic xanthoastrocytoma Complete - CNS5:Subependymal giant cell astrocytoma Incomplete - CNS5:Chordoid glioma Incomplete - CNS5:Astroblastoma, MN1-altered Incomplete Glioneuronal and neuronal tumours - CNS5:Ganglioglioma Incomplete - CNS5:Gangliocytoma Incomplete - CNS5:Desmoplastic infantile ganglioglioma / desmoplastic infantile astrocytoma Incomplete - CNS5:Dysembryoplastic neuroepithelial tumour Incomplete - CNS5:Diffuse glioneuronal tumour with oligodendroglioma-like features and nuclear clusters Incomplete - CNS5:Papillary glioneuronal tumour Incomplete - CNS5:Rosette-forming glioneuronal tumour Incomplete - CNS5:Myxoid glioneuronal tumour Incomplete - CNS5:Diffuse leptomeningeal glioneuronal tumour Incomplete - CNS5:Multinodular and vacuolating neuronal tumour Incomplete - CNS5:Dysplastic cerebellar gangliocytoma (Lhermitte-Duclos disease) Incomplete - CNS5:Central neurocytoma Incomplete - CNS5:Extraventricular neurocytoma Incomplete - CNS5:Cerebellar liponeurocytoma Incomplete Ependymal tumours - CNS5:Supratentorial ependymoma Incomplete - CNS5:Supratentorial ependymoma, ZFTA fusion-positive Incomplete - CNS5:Supratentorial ependymoma, YAP1 fusion-positive Incomplete - CNS5:Posterior fossa ependymoma Incomplete - CNS5:Posterior fossa group A (PFA) ependymoma Incomplete - CNS5:Posterior fossa group B (PFB) ependymoma Incomplete - CNS5:Spinal ependymoma Incomplete - CNS5:Spinal ependymoma, MYCN-amplified Incomplete - CNS5:Myxopapillary ependymoma Incomplete - CNS5:Subependymoma Incomplete
Choroid plexus tumours (Overview Page Link Complete )
- CNS5:Choroid plexus papilloma Incomplete - CNS5:Atypical choroid plexus papilloma Incomplete - CNS5:Choroid plexus carcinoma Incomplete
Embryonal tumours (Overview Page Link Complete )
Medulloblastoma Medulloblastomas, molecularly defined - CNS5:Medulloblastoma, WNT-activated Incomplete - CNS5:Medulloblastoma, SHH-activated and TP53-wildtype Incomplete - CNS5:Medulloblastoma, SHH-activated and TP53-mutant Incomplete - CNS5:Medulloblastoma, non-WNT/non-SHH Incomplete Medulloblastomas, histologically defined - CNS5:Medulloblastoma, histologically defined Incomplete
Other CNS embryonal tumours - CNS5:Atypical teratoid/rhabdoid tumour Incomplete - CNS5:Cribriform neuroepithelial tumour Incomplete - CNS5:Embryonal tumour with multilayered rosettes Incomplete - CNS5:CNS neuroblastoma, FOXR2-activated Incomplete - CNS5:CNS tumour with BCOR internal tandem duplication Incomplete - CNS5:CNS embryonal tumour NEC/NOS Incomplete
Pineal tumours (Overview Page Link Complete )
- CNS5:Pineocytoma Incomplete - CNS5:Pineal parenchymal tumour of intermediate differentiation Incomplete - CNS5:Pineoblastoma Incomplete - CNS5:Papillary tumour of the pineal region Incomplete - CNS5:Desmoplastic myxoid tumour of the pineal region, SMARCB1-mutant Incomplete
Cranial and paraspinal nerve tumours (Overview Page Link Complete )
- CNS5:Schwannoma Incomplete - CNS5:Neurofibroma Incomplete - CNS5:Perineurioma Incomplete - CNS5:Hybrid nerve sheath tumours Incomplete - CNS5:Malignant melanotic nerve sheath tumour Incomplete - CNS5:Malignant peripheral nerve sheath tumour Incomplete - CNS5:Cauda equina neuroendocrine tumour (previously paraganglioma) Incomplete
Meningioma (Overview Page Link Incomplete )
- CNS5:Meningioma Incomplete
Mesenchymal, non-meningothelial tumours involving the CNS (Overview Page Link Complete )
Soft tissue tumours Fibroblastic and myofibroblastic tumours - CNS5:Solitary fibrous tumour Complete Vascular tumours - CNS5:Haemangiomas and vascular malformations Incomplete - CNS5:Haemangioblastoma Incomplete Skeletal muscle tumours - CNS5:Rhabdomyosarcoma Incomplete Tumours of uncertain differentiation - CNS5:Intracranial mesenchymal tumour, FET::CREB fusion-positive Incomplete - CNS5:CIC-rearranged sarcoma Incomplete - CNS5:Primary intracranial sarcoma, DICER1-mutant Incomplete - CNS5:Ewing sarcoma Incomplete
Chondro-osseous tumours Chondrogenic tumours - CNS5:Mesenchymal chondrosarcoma Incomplete - CNS5:Chondrosarcoma Incomplete
Notochordal tumours - CNS5:Chordoma Incomplete
Melanocytic tumours (Overview Page Link Complete )
Diffuse meningeal melanocytic neoplasms - CNS5:Diffuse meningeal melanocytic neoplasms: Melanocytosis and melanomatosis Incomplete Circumscribed meningeal melanocytic neoplasms - CNS5:Circumscribed meningeal melanocytic neoplasms: Melanocytoma and melanoma Incomplete
Haematolymphoid tumours involving the CNS (Overview Page Link Complete )
Lymphomas CNS lymphomas - CNS5:Primary diffuse large B-cell lymphoma of the CNS Incomplete - CNS5:Immunodeficiency-associated CNS lymphomas Incomplete - CNS5:Lymphomatoid granulomatosis Incomplete - CNS5:Intravascular large B-cell lymphoma Incomplete Miscellaneous rare lymphomas in the CNS - CNS5:MALT lymphoma of the dura Incomplete - CNS5:Other low-grade B-cell lymphomas of the CNS Incomplete - CNS5:Anaplastic large cell lymphoma (ALK+/ALK−) Incomplete - CNS5:T-cell and NK/T-cell lymphomas Incomplete
Histiocytic tumours - CNS5:Erdheim-Chester disease Incomplete - CNS5:Rosai-Dorfman disease Incomplete - CNS5:Juvenile xanthogranuloma Complete - CNS5:Langerhans cell histiocytosis Incomplete - CNS5:Histiocytic sarcoma Incomplete
Germ cell tumours (Overview Page Link Complete )
- CNS5:Germ cell tumours of the CNS Incomplete
Tumours of the sellar region (Overview Page Link Complete )
- CNS5:Adamantinomatous craniopharyngioma Incomplete - CNS5:Papillary craniopharyngioma Incomplete - CNS5:Pituicytoma, granular cell tumour of the sellar region, and spindle cell oncocytoma Incomplete - CNS5:Pituitary adenoma / pituitary neuroendocrine tumour Incomplete - CNS5:Pituitary blastoma Incomplete
Metastases to the CNS (Overview Page Link Complete )
- CNS5:Metastases to the brain and spinal cord parenchyma Incomplete - CNS5:Metastases to the meninges Incomplete
Genetic tumour syndromes involving the CNS (Overview Page Link Complete )
- CNS5:Neurofibromatosis type 1 Incomplete - CNS5:Neurofibromatosis type 2 Incomplete - CNS5:Schwannomatosis Incomplete - CNS5:Von Hippel-Lindau syndrome Incomplete - CNS5:Tuberous sclerosis Incomplete - CNS5:Li-Fraumeni syndrome Incomplete - CNS5:Cowden syndrome Incomplete - CNS5:Constitutional mismatch repair deficiency syndrome Incomplete - CNS5:Familial adenomatous polyposis 1 Incomplete - CNS5:Naevoid basal cell carcinoma syndrome Incomplete - CNS5:Rhabdoid tumour predisposition syndrome Incomplete - CNS5:Carney complex Incomplete - CNS5:DICER1 syndrome Incomplete - CNS5:Familial paraganglioma syndromes Incomplete - CNS5:Melanoma-astrocytoma syndrome Incomplete - CNS5:Familial retinoblastoma Incomplete - CNS5:BAP1 tumour predisposition syndrome Incomplete - CNS5:Fanconi anaemia Incomplete - CNS5:ELP1-medulloblastoma syndrome Incomplete